Type I-Hurler’s
- Autosomal recessive.
- Alpha L Iduronidase deficiency.
- Coarse face,Thick skin,severe MR.
- Gargolylism,Corneal opacity.
- Dermatan and Heparan sulfate in urine.
Type -II Hunter’s
- Xlinked recessive.
- Iduronate sulfatase deficiency.
- Mild Hurler’s+aggressive behavior,deafness.
- No corneal opacity.
Mnemonic:Hunter aims for X and has a clear vision
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